Infantile myofibromathosis of the maxilla. A case report

Abstract

Background. Infantile myofibromatosis is a rare benign tumour in children. Its characteristic symptoms are firm masses in soft tissues, bones and visceral organs, and its common locations are head and neck. Three forms are well known: solitary, multicentric and visceral myofibromatosis. All have excellent prognosis, except the last one that may be lethal. Spontaneous regression can occur.

Case report. We present an unusual case of infantile myofibromatosis of the maxilla in an adolescent.

Conclusions. The infantile myofibromatosis should be managed with special caution because of the differential- diagnostic similarity with fibrosarcoma, leomyosarcoma, and histiocytosis.